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Psychological profile of children with Noonan syndrome.

Journal article
Authors D A Lee
S Portnoy
P Hill
Christopher Gillberg
M A Patton
Published in Developmental Medicine and Child Neurology
Volume 47
Issue 1
Pages 35-38
ISSN 0012-1622
Publication year 2005
Published at Institute for the Health of Women and Children, Dept of Child and Adolescent Psychiatry
Pages 35-38
Language en
Links dx.doi.org/10.1111/j.1469-8749.2005...
Keywords Adolescent, Child, Child Behavior Disorders, Diagnosis, Psychology, Child, Preschool, Cohort Studies, England, Female, Follow-Up Studies, Humans, Intelligence, Learning Disorders, Diagnosis, Psychology, Male, Neurologic Examination, Statistics & numerical data, Neuropsychological Tests, Statistics & numerical data, Noonan Syndrome, Diagnosis, Psychology, Personality Inventory, Statistics & numerical data, Psychometrics, Statistics & numerical data, Psychomotor Disorders, Diagnosis, Psychology, Psychomotor Performance, Reference Values, Self Concept, Wechsler Scales
Subject categories Child and adolescent psychiatry

Abstract

A cohort of 48 children with Noonan syndrome, with a mean age of 9 years 10 months (SD 3y 7mo; 28 males, 20 females), was recruited from a national study. Children were assessed using the Wechsler Intelligence Scales and Test of Motor Impairment-Revised (TOMI-R). The Piers-Harris Self-evaluation Questionnaire was also completed in a subgroup of age-appropriate children. Children's parents and teachers completed the Rutter A and B scales to assess of the degree of behavioural and emotional problems respectively. Mean Full-scale IQ score was 84, and one-quarter of the participants had learning disabilities. Verbal IQ tended to be slightly lower than Performance IQ. About half of the group showed evidence of mild to moderate impairment, confirming the impression of 'clumsiness/developmental coordination disorder' on the TOMI-R. Level of self-esteem, as determined by the Piers-Harris Questionnaire, was comparable to that of a standardized population. This research has identified some characteristic psychological features in Noonan syndrome. However, a specific behavioural phenotype could not be identified.

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